eRAM
encyclopedia of Rare Disease Annotation for Precision Medicine
| Disease | cystic fibrosis |
| Comorbidity | C0034069|pulmonary fibrosis |
| Sentences | 4 |
| PubMedID- 20827647 | In end-stage cystic fibrosis and patients with idiopathic pulmonary fibrosis, alternative treatment options are currently not available and lung transplantation is indicated. |
| PubMedID- 24325216 | Copd = chronic obstructive pulmonary disease, cf = cystic fibrosis, a1at = alpha-1antitrypsin deficiency with emphysema, ipf = idiopathic pulmonary fibrosis, pah = pulmonary arterial hypertension, gvhd = graft-versus-host disease. |
| PubMedID- 23523785 | This data identifies ceramide as a key molecule associated with pulmonary fibrosis in cystic fibrosis mice and demonstrate for the first time that prolonged inhibition of acid sphingomyelinase is able to attenuate fibrosis and inflammation in this animal model. |
| PubMedID- 20712568 | They have been focused on chronic obstructive pulmonary disease, acute respiratory distress syndrome, acute lung injury, pulmonary fibrosis, alteration of lung function in cystic fibrosis, as well as asthma and cachexia in lung cancer patients. |
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